This  book is intended as a comprehensive, practically oriented reference on pulmonary  hypertension within the context of adult congenital heart disease (ACHD). After  an introductory chapter on pathophysiology, the various types of pulmonary  hypertension that may be encountered in ACHD are discussed, highlighting the  specifics observed within different patient categories. The diagnostic approach  is then addressed in detail, and the last section of the book is devoted to  management options, from conservative approaches to interventional treatment and  the concept of treat and repair. Management in specific patient subjects, such  as pregnant women, Fontan patients, and Down syndrome patients with Eisenmenger  syndrome, is fully discussed, and guidance is also provided on palliative care.