Having been found in 3%-21% patients with congenital sensorineural deafness, cochlear nerve deficiency (CND) is defined by a small or absent cochlear nerve. This book describes the updated information on the embryology, pre- and post- operative auditory, electrophysiology and vestibular aspects of CND. What s more, the cochlear implantation (CI) strategy and CI outcomes as well as comparison with normal patients will be discussed in details with selected cases and high resolution illustrations. It will be a valuable reference for otologists, audiologists and practitioners who would like to understand more about CND and choose optimal clinical strategy of CI surgery for CND.